Definition: necrotizing, small/medium-vessel vasculitis Symptoms: myalgias, arthralgias, subcutaneous nodules, neuropathy, hematuria Distribution of disease: Renal artery branches (85%) > hepatic artery branches (50%) = small mesenteric branches (50%) Imaging features: microaneurysms Treatment: mainstay is steroids.… Read More »Polyarteritis Nodosa (PAN)
Definition: Post-infectious vasculitis of medium arteries Findings: Coronary artery aneurysms (15%), conjunctivitis, rash, fever ALSO: great vessel aneurysms Kawasaki disease, also known as Kawasaki syndrome, is a rare autoimmune disorder that primarily affects children under… Read More »Kawasaki Disease
Definition: Idiopathic non-necrotizing panarteritis. Demographics: 98% male, 99% smokers Imaging findings: Segmental vascular occlusions, corkscrew vessels, large vessels will appear normal Distribution of disease: Legs & feet | forearms & hands Treatment: stop smoking. This… Read More »Buerger’s Disease (Thromboangiitis Obliterans)
Quick Take on Temporal Arteritis/Giant Cell arteritis (GCA): Nomenclature: Temporal arteritis is also known as Giant cell arteritis (GCA), Horton disease, and cranial arteritis. All of these names refer to the same disease process Demographics:… Read More »Giant Cell Arteritis (Temporal Arteritis)
Etiology: idiopathic, neurofibromatosis, Fibromuscular Dysplasia (FMD), vasculitis, congenital Demographics: Entity seen in children and young adults, presenting with renal failure, juvenile hypertension, or rarely mesenteric ischemia. Imaging findings: Focal stenosis of the juxta-renal aorta with… Read More »Mid-Aortic Syndrome, “Abdominal Coarctation”
Definition: Granulomatous vasculitis of large arteries. Patient population: Mainly young women. F >> M 8:1, 90% age < 30 Symptoms: stroke, asymmetric blood pressures, pain Digital subtraction angiographic findings: Stenosis of the aorta | Great… Read More »Takayasu Arteritis (“Pulseless Disease”)