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Vena Cava Mar 14, 2021

Persistent Left Superior Vena Cava (SVC)

Definition: What is it? Persistent left common cardinal vein Incidence: <1% overall, 3-10% in kids with congenital heart disease. Anatomy: Left brachiocephalic vein often absent. Right SVC is usually present, may be small, rarely absent.…

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Vena Cava Mar 14, 2021

Superior Vena Cava (SVC) Syndrome

Quick Take: Symptoms: facial/neck edema, Jugular vein distention (JVD), headache. Potentially life threatening if progression to laryngeal edema. Etiology/Causes: lung cancer (80%), catheter-related stenosis/thrombosis, fibrosing mediastinitis (histoplasmosis, Tuberculosis (TB), etc.) Contrast Enhanced CT imaging findings:…

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Vasculitis Mar 12, 2021

Polyarteritis Nodosa (PAN)

Definition: necrotizing, small/medium-vessel vasculitis Symptoms: myalgias, arthralgias, subcutaneous nodules, neuropathy, hematuria Distribution of disease: Renal artery branches (85%) > hepatic artery branches (50%) = small mesenteric branches (50%) Imaging features: microaneurysms Treatment: mainstay is steroids.…

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Vasculitis Mar 12, 2021

Kawasaki Disease

Definition: Post-infectious vasculitis of medium arteries Findings: Coronary artery aneurysms (15%), conjunctivitis, rash, fever ALSO: great vessel aneurysms Kawasaki disease, also known as Kawasaki syndrome, is a rare autoimmune disorder that primarily affects children under…

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Vasculitis Mar 12, 2021

Buerger’s Disease (Thromboangiitis Obliterans)

Definition: Idiopathic non-necrotizing panarteritis. Demographics: 98% male, 99% smokers Imaging findings: Segmental vascular occlusions, corkscrew vessels, large vessels will appear normal Distribution of disease: Legs & feet | forearms & hands Treatment: stop smoking. This…

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Vasculitis Mar 12, 2021

Giant Cell Arteritis (Temporal Arteritis)

Quick Take on Temporal Arteritis/Giant Cell arteritis (GCA): Nomenclature: Temporal arteritis is also known as Giant cell arteritis (GCA), Horton disease, and cranial arteritis.  All of these names refer to the same disease process Demographics:…

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Vasculitis Mar 12, 2021

Mid-Aortic Syndrome, “Abdominal Coarctation”

Etiology: idiopathic, neurofibromatosis, Fibromuscular Dysplasia (FMD), vasculitis, congenital Demographics: Entity seen in children and young adults, presenting with renal failure, juvenile hypertension, or rarely mesenteric ischemia. Imaging findings: Focal stenosis of the juxta-renal aorta with…

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Arterial Pathology Mar 10, 2021

Fibromuscular Dysplasia (FMD)

Definition: idiopathic proliferation of fibrous & muscular (fibromuscular!) tissue in medium & large arteries. This is not inflammatory and not atherosclerotic. FMD is the most common cause of Renal artery stenosis (RAS) in children. If…

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